Isolated left ventricular noncompaction in children: two cases with different manifestations.
نویسندگان
چکیده
Isolated noncompaction of the ventricular myocardium is an uncommon disorder characterized by an excessively prominent trabecular meshwork seen in the early period of embryogenesis. The clinical presentation of noncompaction includes a high prevalence of heart failure, thromboembolic events and arrhythmias. Echocardiography is the procedure of choice for the diagnosis of noncompaction. We report two demonstrative patients with isolated noncompaction of the left ventricular myocardium and review the available related literature.
منابع مشابه
Isolated noncompaction of left ventricular myocardium. A study of eight cases.
Isolated noncompaction of left ventricular myocardium is a rare disorder of endomyocardial morphogenesis characterized by numerous, excessively prominent ventricular trabeculations and deep intertrabecular recesses. This study comprised eight cases, including three at necropsy. Ages ranged from 11 months to 22.5 years, with follow-up as long as 5 years. Gross morphological severity ranged from ...
متن کاملClinical features of isolated noncompaction of the ventricular myocardium: long-term clinical course, hemodynamic properties, and genetic background.
OBJECTIVES A nationwide survey was conducted to clarify the clinical features of isolated noncompaction of the ventricular myocardium (INVM) in Japanese children in comparison with features previously described in patients with INVM. BACKGROUND Isolated noncompaction of the ventricular myocardium is a rare disorder characterized by an excessively prominent trabecular meshwork. It is accompani...
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Ventricular noncompaction (VNC) of the myocardium is a rare genetic cardiomyopathy caused by a disorder during endocardial morphogenesis and could be accompanied by life-threatening complications. The major clinical manifestations of VNC are heart failure, arrhythmias, and embolic events. The left ventricle is the most commonly reported affected site, but a few cases of right ventricular involv...
متن کاملResponse to letter regarding article, "mortality and sudden death in pediatric left ventricular noncompaction in a tertiary referral center".
BACKGROUND Left ventricular noncompaction is a cardiomyopathy characterized by excessive trabeculation of the left ventricle, progressive myocardial dysfunction, and early mortality. Left ventricular noncompaction has a heterogeneous clinical presentation that includes arrhythmia and sudden cardiac death. METHODS AND RESULTS We retrospectively reviewed all children diagnosed with left ventric...
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عنوان ژورنال:
- The Eurasian journal of medicine
دوره 40 3 شماره
صفحات -
تاریخ انتشار 2008